NUR 230 Concepts of Nursing the Childbearing Child Caring Family
Exam 4
Question:
sickle cell anemia
Answer:
a genetic disorder that causes abnormal hemoglobin, resulting in some red blood cells assuming an abnormal sickle shape
Hereditary presence of HbS; autosomal recessive trait
Question:
sickle cell anemia diagnostics
Answer:
Newborn screening
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Question:
Sickle Cell Crisis cause
Answer:
infection, stress, dehydration, trauma
Question:
Sickle Cell Crisis types
Answer:
Vaso-occlusive- Splenic sequestration Aplastic
Question:
Vaso-occlusive
Answer:
"painful episode"
Question:
Splenic sequestration -
Answer:
pooling of blood in the spleen 2 / 4
Question:
Aplastic
Answer:
decreased production of RBCs
Question:
what are some complications of sickle cell crisis?
Answer:
Acute chest syndrome CVA
Question:
sickle cell crisis management
Answer:
Oral/IV hydration decrease o2 demands pain management prevent infection splenectomy blood transfusion stem cell transplant
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Question:
sickle cell crisis management: what can be done to prevent infections
Answer:
Immunizations, PCN prophylaxis, hydroxyurea
Question:
sickle cell crisis management: what is considered curative ?
Answer:
Stem cell transplant
Question:
hemophilia is what
Answer:
Bleeding disorder resulting from deficiency or dysfunction of factors (proteins) needed for clotting
Question:
Hemophilia: Pathophysiology
Answer:
Deficiency of factor VIII, produced by liver
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